Source Id |
NCBI (Entrez) Gene Id |
Gene Symbol |
Gene Description |
| ABCB6 |
10058 |
ABCB6 |
ATP binding cassette subfamily B me... |
| ABCB7 |
22 |
ABCB7 |
ATP binding cassette subfamily B me... |
| ABCB8 |
11194 |
ABCB8 |
ATP binding cassette subfamily B me... |
| ABCF2 |
10061 |
ABCF2 |
ATP binding cassette subfamily F me... |
| ACADM |
34 |
ACADM |
acyl-CoA dehydrogenase medium chain... |
| ACN9 |
57001 |
SDHAF3 |
succinate dehydrogenase complex ass... |
| AIFM2 |
84883 |
AIFM2 |
AIF family member 2 [Source:HGNC Sy... |
| AIFM3 |
150209 |
AIFM3 |
AIF family member 3 [Source:HGNC Sy... |
| ALAS2 |
212 |
ALAS2 |
5'-aminolevulinate synthase 2 [Sour... |
| ALDH4A1 |
8659 |
ALDH4A1 |
aldehyde dehydrogenase 4 family mem... |
| ATP5A1 |
498 |
ATP5F1A |
ATP synthase F1 subunit alpha [Sour... |
| ATP5B |
506 |
ATP5F1B |
ATP synthase F1 subunit beta [Sourc... |
| ATP5C1 |
509 |
ATP5F1C |
ATP synthase F1 subunit gamma [Sour... |
| ATP5D |
513 |
ATP5F1D |
ATP synthase F1 subunit delta [Sour... |
| ATP5E |
514 |
ATP5F1E |
ATP synthase F1 subunit epsilon [So... |
| ATP5F1 |
515 |
ATP5PB |
ATP synthase peripheral stalk-membr... |
| ATP5G1 |
516 |
ATP5MC1 |
ATP synthase membrane subunit c loc... |
| ATP5G2 |
517 |
ATP5MC2 |
ATP synthase membrane subunit c loc... |
| ATP5G3 |
518 |
ATP5MC3 |
ATP synthase membrane subunit c loc... |
| ATP5J |
522 |
ATP5PF |
ATP synthase peripheral stalk subun... |
| ATP5O |
539 |
ATP5PO |
ATP synthase peripheral stalk subun... |
| BAX |
581 |
BAX |
BCL2 associated X, apoptosis regula... |
| BCKDHA |
593 |
BCKDHA |
branched chain keto acid dehydrogen... |
| BCKDHB |
594 |
BCKDHB |
branched chain keto acid dehydrogen... |
| BCKDK |
10295 |
BCKDK |
branched chain keto acid dehydrogen... |
| BCL2 |
596 |
BCL2 |
BCL2 apoptosis regulator [Source:HG... |
| BCS1L |
617 |
BCS1L |
BCS1 homolog, ubiquinol-cytochrome ... |
| BNIP3 |
664 |
BNIP3 |
BCL2 interacting protein 3 [Source:... |
| C3orf31 |
132001 |
TAMM41 |
TAM41 mitochondrial translocator as... |
| CASP7 |
840 |
CASP7 |
caspase 7 [Source:HGNC Symbol;Acc:H... |
| CASQ1 |
844 |
CASQ1 |
calsequestrin 1 [Source:HGNC Symbol... |
| CENTA2 |
55803 |
ADAP2 |
ArfGAP with dual PH domains 2 [Sour... |
| COX15 |
1355 |
COX15 |
cytochrome c oxidase assembly homol... |
| COX18 |
285521 |
COX18 |
cytochrome c oxidase assembly facto... |
| COX6B2 |
125965 |
COX6B2 |
cytochrome c oxidase subunit 6B2 [S... |
| CS |
1431 |
CS |
citrate synthase [Source:HGNC Symbo... |
| CYCS |
54205 |
CYCS |
cytochrome c, somatic [Source:HGNC ... |
| DBT |
1629 |
DBT |
dihydrolipoamide branched chain tra... |
| DNAJA3 |
9093 |
DNAJA3 |
DnaJ heat shock protein family (Hsp... |
| ETFA |
2108 |
ETFA |
electron transfer flavoprotein subu... |
| ETFB |
2109 |
ETFB |
electron transfer flavoprotein subu... |
| FIS1 |
51024 |
FIS1 |
fission, mitochondrial 1 [Source:HG... |
| GATM |
2628 |
GATM |
glycine amidinotransferase [Source:... |
| GRPEL1 |
80273 |
GRPEL1 |
GrpE like 1, mitochondrial [Source:... |
| HADHB |
3032 |
HADHB |
hydroxyacyl-CoA dehydrogenase trifu... |
| HCCS |
3052 |
HCCS |
holocytochrome c synthase [Source:H... |
| HSD3B1 |
3283 |
HSD3B1 |
hydroxy-delta-5-steroid dehydrogena... |
| HSD3B2 |
3284 |
HSD3B2 |
hydroxy-delta-5-steroid dehydrogena... |
| HTRA2 |
27429 |
HTRA2 |
HtrA serine peptidase 2 [Source:HGN... |
| IMMT |
10989 |
IMMT |
inner membrane mitochondrial protei... |
| KIAA1967 |
57805 |
CCAR2 |
cell cycle and apoptosis regulator ... |
| MAOB |
4129 |
MAOB |
monoamine oxidase B [Source:HGNC Sy... |
| MARS2 |
92935 |
MARS2 |
methionyl-tRNA synthetase 2, mitoch... |
| MCL1 |
4170 |
MCL1 |
MCL1 apoptosis regulator, BCL2 fami... |
| MFN2 |
9927 |
MFN2 |
mitofusin 2 [Source:HGNC Symbol;Acc... |
| MPV17 |
4358 |
MPV17 |
mitochondrial inner membrane protei... |
| MRPL10 |
124995 |
MRPL10 |
mitochondrial ribosomal protein L10... |
| MRPL12 |
6182 |
MRPL12 |
mitochondrial ribosomal protein L12... |
| MRPL23 |
6150 |
MRPL23 |
mitochondrial ribosomal protein L23... |
| MRPL32 |
64983 |
MRPL32 |
mitochondrial ribosomal protein L32... |
| MRPL40 |
64976 |
MRPL40 |
mitochondrial ribosomal protein L40... |
| MRPL41 |
64975 |
MRPL41 |
mitochondrial ribosomal protein L41... |
| MRPL42 |
28977 |
MRPL42 |
mitochondrial ribosomal protein L42... |
| MRPL51 |
51258 |
MRPL51 |
mitochondrial ribosomal protein L51... |
| MRPL52 |
122704 |
MRPL52 |
mitochondrial ribosomal protein L52... |
| MRPL55 |
128308 |
MRPL55 |
mitochondrial ribosomal protein L55... |
| MRPS10 |
55173 |
MRPS10 |
mitochondrial ribosomal protein S10... |
| MRPS11 |
64963 |
MRPS11 |
mitochondrial ribosomal protein S11... |
| MRPS12 |
6183 |
MRPS12 |
mitochondrial ribosomal protein S12... |
| MRPS15 |
64960 |
MRPS15 |
mitochondrial ribosomal protein S15... |
| MRPS16 |
51021 |
MRPS16 |
mitochondrial ribosomal protein S16... |
| MRPS18A |
55168 |
MRPS18A |
mitochondrial ribosomal protein S18... |
| MRPS18C |
51023 |
MRPS18C |
mitochondrial ribosomal protein S18... |
| MRPS21 |
54460 |
MRPS21 |
mitochondrial ribosomal protein S21... |
| MRPS22 |
56945 |
MRPS22 |
mitochondrial ribosomal protein S22... |
| MRPS24 |
64951 |
MRPS24 |
mitochondrial ribosomal protein S24... |
| MRPS28 |
28957 |
MRPS28 |
mitochondrial ribosomal protein S28... |
| MRPS35 |
60488 |
MRPS35 |
mitochondrial ribosomal protein S35... |
| MRPS36 |
92259 |
KGD4 |
alpha-ketoglutarate dehydrogenase s... |
| MSTO1 |
55154 |
MSTO1 |
misato mitochondrial distribution a... |
| MTX2 |
10651 |
MTX2 |
metaxin 2 [Source:HGNC Symbol;Acc:H... |
| ND1 |
4535 |
MT-ND1 |
mitochondrially encoded NADH:ubiqui... |
| NDUFA1 |
4694 |
NDUFA1 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFA13 |
51079 |
NDUFA13 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFA2 |
4695 |
NDUFA2 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFA6 |
4700 |
NDUFA6 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFA9 |
4704 |
NDUFA9 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFAB1 |
4706 |
NDUFAB1 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFB6 |
4712 |
NDUFB6 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFS1 |
4719 |
NDUFS1 |
NADH:ubiquinone oxidoreductase core... |
| NDUFS2 |
4720 |
NDUFS2 |
NADH:ubiquinone oxidoreductase core... |
| NDUFS3 |
4722 |
NDUFS3 |
NADH:ubiquinone oxidoreductase core... |
| NDUFS4 |
4724 |
NDUFS4 |
NADH:ubiquinone oxidoreductase subu... |
| NDUFS7 |
374291 |
NDUFS7 |
NADH:ubiquinone oxidoreductase core... |
| NDUFS8 |
4728 |
NDUFS8 |
NADH:ubiquinone oxidoreductase core... |
| NDUFV1 |
4723 |
NDUFV1 |
NADH:ubiquinone oxidoreductase core... |
| NFS1 |
9054 |
NFS1 |
NFS1 cysteine desulfurase [Source:H... |
| NNT |
23530 |
NNT |
nicotinamide nucleotide transhydrog... |
| NR3C1 |
2908 |
NR3C1 |
nuclear receptor subfamily 3 group ... |
| OGDH |
4967 |
OGDH |
oxoglutarate dehydrogenase [Source:... |
| OPA1 |
4976 |
OPA1 |
OPA1 mitochondrial dynamin like GTP... |
| OXA1L |
5018 |
OXA1L |
OXA1L mitochondrial inner membrane ... |
| PHB |
5245 |
PHB1 |
prohibitin 1 [Source:HGNC Symbol;Ac... |
| PHB2 |
11331 |
PHB2 |
prohibitin 2 [Source:HGNC Symbol;Ac... |
| PIN4 |
5303 |
PIN4 |
peptidylprolyl cis/trans isomerase,... |
| PITRM1 |
10531 |
PITRM1 |
pitrilysin metallopeptidase 1 [Sour... |
| PMPCA |
23203 |
PMPCA |
peptidase, mitochondrial processing... |
| POLG2 |
11232 |
POLG2 |
DNA polymerase gamma 2, accessory s... |
| PPOX |
5498 |
PPOX |
protoporphyrinogen oxidase [Source:... |
| RAB11FIP5 |
26056 |
RAB11FIP5 |
RAB11 family interacting protein 5 ... |
| RAF1 |
5894 |
RAF1 |
Raf-1 proto-oncogene, serine/threon... |
| RHOT1 |
55288 |
RHOT1 |
ras homolog family member T1 [Sourc... |
| RHOT2 |
89941 |
RHOT2 |
ras homolog family member T2 [Sourc... |
| SDHA |
6389 |
SDHA |
succinate dehydrogenase complex fla... |
| SDHD |
6392 |
SDHD |
succinate dehydrogenase complex sub... |
| SLC25A1 |
6576 |
SLC25A1 |
solute carrier family 25 member 1 [... |
| SLC25A11 |
8402 |
SLC25A11 |
solute carrier family 25 member 11 ... |
| SLC25A15 |
10166 |
SLC25A15 |
solute carrier family 25 member 15 ... |
| SLC25A22 |
79751 |
SLC25A22 |
solute carrier family 25 member 22 ... |
| SLC25A3 |
5250 |
SLC25A3 |
solute carrier family 25 member 3 [... |
| SLC25A6 |
293 |
SLC25A6 |
solute carrier family 25 member 6 [... |
| SUPV3L1 |
6832 |
SUPV3L1 |
Suv3 like RNA helicase [Source:HGNC... |
| SURF1 |
6834 |
SURF1 |
SURF1 cytochrome c oxidase assembly... |
| TFB2M |
64216 |
TFB2M |
transcription factor B2, mitochondr... |
| TIMM10 |
26519 |
TIMM10 |
translocase of inner mitochondrial ... |
| TIMM13 |
26517 |
TIMM13 |
translocase of inner mitochondrial ... |
| TIMM17A |
10440 |
TIMM17A |
translocase of inner mitochondrial ... |
| TIMM17B |
10245 |
TIMM17B |
translocase of inner mitochondrial ... |
| TIMM23 |
100287932 |
TIMM23 |
translocase of inner mitochondrial ... |
| TIMM44 |
10469 |
TIMM44 |
translocase of inner mitochondrial ... |
| TIMM50 |
92609 |
TIMM50 |
translocase of inner mitochondrial ... |
| TIMM8B |
26521 |
TIMM8B |
translocase of inner mitochondrial ... |
| TIMM9 |
26520 |
TIMM9 |
translocase of inner mitochondrial ... |
| TOMM22 |
56993 |
TOMM22 |
translocase of outer mitochondrial ... |
| TOMM34 |
10953 |
TOMM34 |
translocase of outer mitochondrial ... |
| UCP3 |
7352 |
UCP3 |
uncoupling protein 3 [Source:HGNC S... |
| UQCRB |
7381 |
UQCRB |
ubiquinol-cytochrome c reductase bi... |
| UQCRC1 |
7384 |
UQCRC1 |
ubiquinol-cytochrome c reductase co... |
| UQCRH |
7388 |
UQCRH |
ubiquinol-cytochrome c reductase hi... |
| VDAC1 |
7416 |
VDAC1 |
voltage dependent anion channel 1 [... |
| VDAC2 |
7417 |
VDAC2 |
voltage dependent anion channel 2 [... |
| VDAC3 |
7419 |
VDAC3 |
voltage dependent anion channel 3 [... |