Source Id | 
            NCBI (Entrez) Gene Id | 
            Gene Symbol | 
            Gene Description | 
          
          
            
              | 1373 | 
              1373 | 
              CPS1 | 
              carbamoyl-phosphate synthase 1 [Source:HGNC Symb... | 
            
          
            
              | 1891 | 
              1891 | 
              ECH1 | 
              enoyl-CoA hydratase 1 [Source:HGNC Symbol;Acc:HG... | 
            
          
            
              | 1892 | 
              1892 | 
              ECHS1 | 
              enoyl-CoA hydratase, short chain 1 [Source:HGNC ... | 
            
          
            
              | 1962 | 
              1962 | 
              EHHADH | 
              enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydr... | 
            
          
            
              | 2271 | 
              2271 | 
              FH | 
              fumarate hydratase [Source:HGNC Symbol;Acc:HGNC:... | 
            
          
            
              | 2746 | 
              2746 | 
              GLUD1 | 
              glutamate dehydrogenase 1 [Source:HGNC Symbol;Ac... | 
            
          
            
              | 275 | 
              275 | 
              AMT | 
              aminomethyltransferase [Source:HGNC Symbol;Acc:H... | 
            
          
            
              | 3030 | 
              3030 | 
              HADHA | 
              hydroxyacyl-CoA dehydrogenase trifunctional mult... | 
            
          
            
              | 3032 | 
              3032 | 
              HADHB | 
              hydroxyacyl-CoA dehydrogenase trifunctional mult... | 
            
          
            
              | 3034 | 
              3034 | 
              HAL | 
              histidine ammonia-lyase [Source:HGNC Symbol;Acc:... | 
            
          
            
              | 34 | 
              34 | 
              ACADM | 
              acyl-CoA dehydrogenase medium chain [Source:HGNC... | 
            
          
            
              | 36 | 
              36 | 
              ACADSB | 
              acyl-CoA dehydrogenase short/branched chain [Sou... | 
            
          
            
              | 37 | 
              37 | 
              ACADVL | 
              acyl-CoA dehydrogenase very long chain [Source:H... | 
            
          
            
              | 48 | 
              48 | 
              ACO1 | 
              aconitase 1 [Source:HGNC Symbol;Acc:HGNC:117] | 
            
          
            
              | 50 | 
              50 | 
              ACO2 | 
              aconitase 2 [Source:HGNC Symbol;Acc:HGNC:118] | 
            
          
            
              | 5092 | 
              5092 | 
              PCBD1 | 
              pterin-4 alpha-carbinolamine dehydratase 1 [Sour... | 
            
          
            
              | 5805 | 
              5805 | 
              PTS | 
              6-pyruvoyltetrahydropterin synthase [Source:HGNC... | 
            
          
            
              | 7390 | 
              7390 | 
              UROS | 
              uroporphyrinogen III synthase [Source:HGNC Symbo... | 
            
          
            
              | 760 | 
              760 | 
              CA2 | 
              carbonic anhydrase 2 [Source:HGNC Symbol;Acc:HGN... | 
            
          
            
              | 762 | 
              762 | 
              CA4 | 
              carbonic anhydrase 4 [Source:HGNC Symbol;Acc:HGN... | 
            
          
            
              | 763 | 
              763 | 
              CA5A | 
              carbonic anhydrase 5A [Source:HGNC Symbol;Acc:HG... | 
            
          
            
              | 765 | 
              765 | 
              CA6 | 
              carbonic anhydrase 6 [Source:HGNC Symbol;Acc:HGN... | 
            
          
            
              | 767 | 
              767 | 
              CA8 | 
              carbonic anhydrase 8 [Source:HGNC Symbol;Acc:HGN... | 
            
          
            
              | 770 | 
              770 | 
              CA11 | 
              carbonic anhydrase 11 [Source:HGNC Symbol;Acc:HG... | 
            
          
            
              | 875 | 
              875 | 
              CBS | 
              cystathionine beta-synthase [Source:HGNC Symbol;... |